Eosinophilic Fasciitis: A Rare Skin Sclerosis

نویسندگان

  • Amandine Servy
  • Thierry Clérici
  • Caroline Malines
  • Jean-Marie Le Parc
  • Jean-François Côté
چکیده

Eosinophilic fasciitis (Schulman's syndrome) is a rare disease with specific clinical symptoms such as the groove sign which facilitate diagnosis. We report a typical case of eosinophilic fasciitis in an otherwise healthy 49-year-old man who presented with "prayer and groove signs". Histological analysis showed sclerosis and eosinophilic infiltration of the fascia. The patient was successfully treated with systemic corticotherapy and Cyclosporine. A short review of the clinicopathological features of the lesions is presented.

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عنوان ژورنال:

دوره 2011  شماره 

صفحات  -

تاریخ انتشار 2010